1567 muscle ultrastructure and histochemistry in reye's syndrome

1567 muscle ultrastructure and histochemistry in reye's syndrome

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ABSTRACT Muscle histochemistry and ultrastructure was studied on percutaneous muscle biopsies from 3 patients with Reye's syndrome 3, 11 and 14 years old. Two or 3 sequential samples were obtained from each patient using 4.0 and 5.0 mm Bergstrom needles. No complications were observed in spite of prolonged PT and PTT. H & E sections were normal but significant lipid accumulation was seen on oil red 0 stained sections of tissue obtained between the first and tenth days of illness. The lipid was distributed fairly evenly throughout type I muscle fibers. Lipid content decreased slowly and was normal after about 6 weeks. Oxidative enzyme and other histochemical stains (NADH, succinic dehydrogenase, ATPase, acid phosphatase, modified trichrome) were normal. The major ultrastructural abnormality observed was loss of cristae in most mitochondria along with vacuolization and pleomorphic shapes. Lipid vacuoles were prominent in the cytoplasm. One biopsy revealed numerous electron-dense crystalline arrays of 100-120 A particles, similar in appearance to virus particles. Ultrastructural changes returned to normal after several weeks. Lipid accumulation and mitochondrial abnormalities in muscle tissue closely parallel those seen in liver tissue. Percutaneous muscle biopsy appears to be a safe and effective technique for the diagnosis of Reye's syndrome. ARTICLE PDF AUTHOR INFORMATION AUTHORS AND AFFILIATIONS * Departments of Pediatrics, Emanuel Hospital and University of Oregon Health Sciences Center, Portland, Oregon John H Di Liberti & Robert C Neerhout Authors * John H Di Liberti View author publications You can also search for this author inPubMed Google Scholar * Robert C Neerhout View author publications You can also search for this author inPubMed Google Scholar RIGHTS AND PERMISSIONS Reprints and permissions ABOUT THIS ARTICLE CITE THIS ARTICLE Di Liberti, J., Neerhout, R. 1567 MUSCLE ULTRASTRUCTURE AND HISTOCHEMISTRY IN REYE'S SYNDROME. _Pediatr Res_ 15 (Suppl 4), 704 (1981). https://doi.org/10.1203/00006450-198104001-01584 Download citation * Issue Date: 01 April 1981 * DOI: https://doi.org/10.1203/00006450-198104001-01584 SHARE THIS ARTICLE Anyone you share the following link with will be able to read this content: Get shareable link Sorry, a shareable link is not currently available for this article. Copy to clipboard Provided by the Springer Nature SharedIt content-sharing initiative

ABSTRACT Muscle histochemistry and ultrastructure was studied on percutaneous muscle biopsies from 3 patients with Reye's syndrome 3, 11 and 14 years old. Two or 3 sequential samples


were obtained from each patient using 4.0 and 5.0 mm Bergstrom needles. No complications were observed in spite of prolonged PT and PTT. H & E sections were normal but significant lipid


accumulation was seen on oil red 0 stained sections of tissue obtained between the first and tenth days of illness. The lipid was distributed fairly evenly throughout type I muscle fibers.


Lipid content decreased slowly and was normal after about 6 weeks. Oxidative enzyme and other histochemical stains (NADH, succinic dehydrogenase, ATPase, acid phosphatase, modified


trichrome) were normal. The major ultrastructural abnormality observed was loss of cristae in most mitochondria along with vacuolization and pleomorphic shapes. Lipid vacuoles were prominent


in the cytoplasm. One biopsy revealed numerous electron-dense crystalline arrays of 100-120 A particles, similar in appearance to virus particles. Ultrastructural changes returned to normal


after several weeks. Lipid accumulation and mitochondrial abnormalities in muscle tissue closely parallel those seen in liver tissue. Percutaneous muscle biopsy appears to be a safe and


effective technique for the diagnosis of Reye's syndrome. ARTICLE PDF AUTHOR INFORMATION AUTHORS AND AFFILIATIONS * Departments of Pediatrics, Emanuel Hospital and University of Oregon


Health Sciences Center, Portland, Oregon John H Di Liberti & Robert C Neerhout Authors * John H Di Liberti View author publications You can also search for this author inPubMed Google


Scholar * Robert C Neerhout View author publications You can also search for this author inPubMed Google Scholar RIGHTS AND PERMISSIONS Reprints and permissions ABOUT THIS ARTICLE CITE THIS


ARTICLE Di Liberti, J., Neerhout, R. 1567 MUSCLE ULTRASTRUCTURE AND HISTOCHEMISTRY IN REYE'S SYNDROME. _Pediatr Res_ 15 (Suppl 4), 704 (1981).


https://doi.org/10.1203/00006450-198104001-01584 Download citation * Issue Date: 01 April 1981 * DOI: https://doi.org/10.1203/00006450-198104001-01584 SHARE THIS ARTICLE Anyone you share the


following link with will be able to read this content: Get shareable link Sorry, a shareable link is not currently available for this article. Copy to clipboard Provided by the Springer


Nature SharedIt content-sharing initiative